ISSN 1308-8734 | E-ISSN 1308-8742
Case Report
Cystic Lung Disease in Birt-Hogg-Dubé Syndrome: A Case Series of Three Patients
1 Department of Radiology, Hacettepe University Faculty of Medicine, Ankara, Turkey  
2 Department of Radiology, Pamukkale University Hospital, Denizli, Turkey  
Eurasian J Med 2014; 46: 138-141
DOI: 10.5152/eajm.2014.31
Key Words: Birt-Hogg-Dubé syndrome, chest CT, lung cyst
Abstract

Birt-Hogg-Dubé syndrome is characterized by clinical manifestations such as hamartomas of the skin, renal tumors and lung cysts with spontaneous pneumothoraces. Patients with Birt-Hogg-Dubé syndrome may present with only multiple lung cysts. We report the chest computerized tomography (CT) features of three patients with Birt-Hogg-Dubé syndrome. Each patient had multiple lung cysts of various sizes according to chest CT evaluation, most of which were located in lower lobes and related to pleura. The identification of unique characteristics in the chest CT of patients with Birt-Hogg-Dubé syndrome may provide an efficient mechanism for diagnosis. 

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